Other signs and symptoms of this disease is urine or sweat that smells of maple syrup, diffuculty concentrating, lethargy, vomiting, seizures and death. Sweet-smelling urine can also indicate diabetes mellitus, because excess blood sugar finds its way into the urine. This condition causes the urine of an infant to have a distinct, sweet, maple syrup-like odor. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the body's inability to digest certain amino acids. So I Googled it and only find a few people posting the honest question, maybe one or two honest answers and then the thread of absurdities. So many things can make your urine smell like eggs or sulfur. Not just like something sweet. Urine smells like cough syrup . My kidneys started to hurt slightly from time to time, so I quit drinking. MSUD is caused by genetic variants in the BCKDHA, BCKDHB, or DBT genes. Maple syrupe urine disease (MSUD) is an autosomal recessive metabolic disorder that leads to the accumulation of branched-chain amino acids. The last few years I have been drinking Coke every day -- 1-3 cans/day. I'd think a maple syrup smelling pig is much more desirable than a stinky smelling pig! Charlie: Well, it’s the bedroom-Tom: Those smell questions are tough. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the … About 2 months ago, I swore my urine {a little darker than usual that day} smelled like it. Among worldwide Maple syrup urine disease (MSUD) affects about 1 out of 185,000 babies. The symptoms of other forms of MSUD start in adolescence or adulthood. Early treatment is vital. An inherited condition, maple syrup urine disease, so named because it causes urine to smell like sweet maple syrup, results from the body's inability to digest certain amino acids. my cat smells like maple syrup. The infant is usually lethargic, feeds poorly, vomits and has a developmental delay. Then I go days without smelling it. There is metabolic condition which causes urine to smell like maple syrup. There's a disease in humans called maple syrup urine disease caused by a defect in a metabolic enzyme required to break down branched chain amino acids... Could possibly occur in a cat? Diagnosis of MSUD is based on the symptoms, clinical exam, and blood and urine testing. Cat urine that’s outside the litter box is usually unnoticed until it becomes a problem. It is caused by a defect in 1 of 3 genes. My pee smells like maple syrup!!! MD. Then, Rachel unexplainably goes into a coma, but fortunately, doctors are able to diagnose her with maple syrup urine disease (MSUD). It's not both underarms every time either, might be just one or the other that day. C. Lybol, DEM (midwife) 1 mom found this helpful I think my cat has been lying or rolling in some aromatic plants or weeds nearby. Urine, sweat, or earwax that smells like maple syrup or burnt sugar. Please go in right away. The result is your pee smells like maple syrup as the chemical buildup from undigested leucine, isoleucine, and valine changes how your urine smells. That smell could be due to one of the following reasons: 1. Excessive levels of sugar in the urine can also cause it to smell of maple syrup, though this is often described as a more sickly-sweet smell. Premium Questions. It still smells like maple syrup. level 1. I read something about Maple Sypup Urine Disease but he says that his urine does not smell like that. It is usually picked up on the metabolic screen the state does on newborns. If you notice your dog’s urine is smells like maple syrup, it could be a sign of canine diabetes. Pills like Oxycontin or Percocet give off a sweet smell as they burn. It is inherited in an autosomal recessive pattern. My dog is a shiba, and they're the cats of the dog world, so maybe that's it! dog smells like fritos. Once discovered, the baby is given a protein free diet that it … But, your baby may have been missed. What could be causing this? Original Poster 1 year ago. It's usually discovered at an early age because of the fact the the baby's urine smells like maple syrup. A: If you notice a very distinct sweet smell as you urinate, this could mean one of two things: maple syrup urine disease or diabetic ketoacidosis (DKA). There is a disease called Maple Syrup Urine Disease, no joke...but infants are tested for it and I don't know if you can even develop it later in life. Genetic and Rare Diseases Information Center (GARD) - PO Box 8126, Gaithersburg, MD 20898-8126 - Toll-free: 1-888-205-2311 You probably don’t have maple syrup urine disease because it’s a rare inherited disorder that affects an estimated 1 in 185,000 infants worldwide, according to the National Institutes of Health. This may not always be present in all types. Q: Why does my urine smell like maple syrup? Causes. Unless you know for sure that they only smell because of an isolated potty accident, having the underlying issue diagnosed is the best move. 8. The urine smell could be the result of what you are eating. My spayed 1 year old cat has started smelling like maple syrup. A rare genetic condition, maple syrup urine disease causes problems with breaking down some amino acids in the proteins you consume. Absolutely, but as far as that goes, I’d investigate the walls. shes totally healthy. Cat urine is not all that different from other animals’ urine, but what gives cat urine such a bad smell? The bedroom, the closet and … It … Urine Smells Like Eggs: Causes. Asparagus is a good example. We use cookies to give you the best possible experience on our website. My cat smells like maple syrup too. I just noticed that my boyfriends sweat smells like maple syrup. Maple Syrup Urine Disease. So many foods can be responsible for making your urine smell like eggs. MSUD is more common in certain ethnic groups but also it is seen in many countries. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. The urine of people with this condition can smell like maple syrup. Research studies show that about 1 out of every 380 babies from the Old Order Mennonite population is affected by this condition. Species:Cat. People with this disorder aren't meant to eat protein, meaning this is the one, single good reason to go vegan. Opiates are typically the only kind of pills that are smoked. Maple syrup urine disease. Info please on maple sugar urine disease~what foods to avoid ~have 14 mo old who tested neg for PKU @ birth and today has maple smelling urine. There can also be cases where your dog actually smells like maple syrup or their urine is foamy, both signs of possible trouble that shouldn’t be ignored. Strange smells. Changes in muscle tone – poor muscle tone, muscle tightness/tension Seriously-pancake syrup. Maple syrup urine disease (MSUD) is a rare, inherited metabolic disorder. I have let this machine run for hours . I don’t know why something would smell like maple syrup in a house that is constructed like it is. We started looking for the GI problems in November-so it wasn't long after that. The type of Freon is R410A some say it a leak. Luna, She doesn't like wet food - Answered by a verified Cat Veterinarian. If you do have this disease it is very serious and you need to be seen by a doctor immediately. The earwax and urine of infants with MSUD smells like maple syrup. Diet. Sweat and urine smells like maple syrup; milk and/or breastfed baby may smell like maple syrup. Why does my dog’s urine smell like maple syrup? I am 17 -- 5' 10'' -- 128lbs. level 2. This leads to a buildup of these chemicals in the blood. I switched to coffee because I have severe withdrawal if I don't get any caffeine. Why? Suggest treatment for maple syrup urine disease . Charlie: Yeah. … My cat's pee smells like syrup, but I just took him to the vet and got his blood and urine tested and he's healthy. Sweet-Smelling Urine Medically reviewed by Alana Biggers, M.D., MPH Find out why your urine smells sweet or fruity, what’s causing this symptom, and treatment methods. Poor feeding, vomiting, loss of appetite, irritability. Use of more than 100 grams of fenugreek seeds daily can cause intestinal distress and nausea (recommended dose is less than 8 grams per day). Maple syrup urine disease (MSUD) is a disorder in which the body cannot break down certain parts of proteins. Sweet-smelling urine can also indicate diabetes mellitus, because excess blood sugar finds its way into the urine. In humans there is a disease called maple syrup urine disease where one of the signs is a sweet syrup smell to urine. Cat Urine Gets Worse With Time. If you have problems viewing PDF files, download the latest version of Adobe Reader. MD. Is Lupituss syrup safe to take for dry cough? Occasionally causes loose stools, which go away when fenugreek is discontinued. Additional Reading: 7 Steps to Take … Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. Want to know more about maple syrup urine disease and its symptoms? Since Rachel Webb was born, she has had urine that smells like maple syrup, cries constantly for no reason, has feeding problems, and has bouts of unresponsiveness. (This disorder got its name from this common symptom.) lol. Users frequently say the smoke tastes and smells like sugar and burnt marshmallows. Maple syrup urine disease is a metabolic disorder that causes certain amino acids to build up in … 1. share. I drink 1 large mug of coffee every day. Report Save. Fritos seem to be the universal dog smell. What is maple syrup urine odor Honey vs sugar vs maple syrup Connect by text or video with a U.S. board-certified doctor now — wait time is less than 1 minute! For language access assistance, contact the NCATS Public Information Officer. Does diabetes run in you family? Maple syrup urine disease or ketoacidemia is an inherited disorder, where the body lacks certain enzymes that break down amino acids. Report Save. He told me that it has for a very long time and he never knew why. Do you mysteriously smell maple syrup everywhere? 2. share. The disease prevents your body from breaking down certain amino acids. Sluggish/slow/tiredness and weakness. Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. The urine smell like maple syrup, it ’ s urine is smells like maple.... State does on newborns know why something would smell like maple syrup called maple syrup urine disease ( ). 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